| Disease ID | Source | Name | Description |
| 225280 | OMIM | Ectodermal dysplasia, ectrodactyly, and macular dystrophy syndrome (EEMS) | A form of ectodermal dysplasia, a heterogeneous group of disorders due to abnormal development of two or more ectodermal structures. It is an autosomal recessive condition characterized by features of ectodermal dysplasia such as sparse eyebrows and scalp hair, and selective tooth agenesis associated with macular dystrophy and ectrodactyly. The disease is caused by variants affecting the gene represented in this entry. |
| 601553 | OMIM | Hypotrichosis congenital with juvenile macular dystrophy (HJMD) | A disorder characterized by congenital hypotrichosis, early hair loss, and severe degenerative changes of the retinal macula that culminate in blindness during the second to third decade of life. The disease is caused by variants affecting the gene represented in this entry. |