Entity Details

Primary name ATX3_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionP54252
EntryNameATX3_HUMAN
FullNameAtaxin-3
TaxID9606
Evidenceevidence at protein level
Length361
SequenceStatuscomplete
DateCreated1996-10-01
DateModified2021-06-02

Ontological Relatives

GenesATXN3

GO terms

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GOName
GO:0000226 microtubule cytoskeleton organization
GO:0004843 thiol-dependent deubiquitinase
GO:0005634 nucleus
GO:0005654 nucleoplasm
GO:0005730 nucleolus
GO:0005737 cytoplasm
GO:0005759 mitochondrial matrix
GO:0005829 cytosol
GO:0005886 plasma membrane
GO:0006289 nucleotide-excision repair
GO:0006511 ubiquitin-dependent protein catabolic process
GO:0006515 protein quality control for misfolded or incompletely synthesized proteins
GO:0007268 chemical synaptic transmission
GO:0007399 nervous system development
GO:0010810 regulation of cell-substrate adhesion
GO:0016363 nuclear matrix
GO:0016579 protein deubiquitination
GO:0030036 actin cytoskeleton organization
GO:0031625 ubiquitin protein ligase binding
GO:0031966 mitochondrial membrane
GO:0034605 cellular response to heat
GO:0035520 monoubiquitinated protein deubiquitination
GO:0042405 nuclear inclusion body
GO:0042802 identical protein binding
GO:0043161 proteasome-mediated ubiquitin-dependent protein catabolic process
GO:0045104 intermediate filament cytoskeleton organization
GO:0045202 synapse
GO:0051117 ATPase binding
GO:0061578 Lys63-specific deubiquitinase activity
GO:0070536 protein K63-linked deubiquitination
GO:0071108 protein K48-linked deubiquitination
GO:0071218 cellular response to misfolded protein
GO:1904294 positive regulation of ERAD pathway
GO:1904379 protein localization to cytosolic proteasome complex involved in ERAD pathway
GO:1990380 Lys48-specific deubiquitinase activity

Subcellular Location

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Subcellular Location
Nucleus
Nucleus matrix

Domains

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DomainNameCategoryType
IPR003903 Ubiquitin interacting motifSiteConserved site
IPR006155 Josephin domainDomainDomain
IPR033865 Machado-Joseph disease proteinFamilyFamily

Diseases

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Interactions

182 interactions

InteractorPartnerSourcesPublicationsLink
ATX3_HUMANUBC_HUMANBioGRID, MINT12857950 14559776 14602712 16040601 16118278 16196087 18599482 19153604 20622874 20865150 21118805 23314748 23625928 23659897 25144244 25231079 25448680 25527291 25988170 28190767 28918024 29576527 29661116 30455355 details
ATX3_HUMANPSMD7_HUMANBioGRID, HPRD, IntAct, MINT12944474 30455355 32814053 details
ATX3_HUMANTERA_HUMANBioGRID, HPRD, IntAct, MINT12944474 14749733 16525503 16822850 18199748 19175675 19843543 20414249 22970133 23383273 24100225 25231079 27762274 27851749 28180282 28275011 28939772 29540532 30455355 32814053 details
ATX3_HUMANEWS_HUMANBioGRID, HPRD, IntAct16713569 32814053 details
ATX3_HUMANRHG19_HUMANBioGRID, HPRD, IntAct16713569 32814053 details
ATX3_HUMANPHAF1_HUMANBioGRID, HPRD, IntAct16713569 32814053 details
ATX3_HUMANRD23A_HUMANBioGRID, HPRD, IntAct10915768 16712842 16713569 17935801 19013454 22970133 30455355 32296183 32814053 details
ATX3_HUMANRD23B_HUMANBioGRID, HPRD, IntAct, MINT10915768 16712842 16713569 19843543 30455355 details
ATX3_HUMANPICK1_HUMANBioGRID, HPRD, IntAct16713569 details
ATX3_HUMANATX3_HUMANBioGRID, MINT16194547 16525503 21780213 22129356 details
ATX3_HUMANUBE4B_HUMANBioGRID, MINT14749733 16525503 details
ATX3_HUMANUBQL1_HUMANBioGRID, HPRD, IntAct, MINT17082820 32814053 details
ATX3_HUMANOTUB2_HUMANBioGRID, IntAct19615732 32814053 details
ATX3_HUMANUBP13_HUMANBioGRID, IntAct19615732 32814053 details
ATX3_HUMANANXA7_HUMANBioGRID, MINT21900206 details
ATX3_HUMANCDN1A_HUMANBioGRID, MINT21900206 details
ATX3_HUMANDYN2_HUMANBioGRID, IntAct, MINT21900206 32814053 details
ATX3_HUMANGSK3B_HUMANBioGRID, MINT17434145 21900206 details
ATX3_HUMANMKNK1_HUMANBioGRID, MINT21900206 details
ATX3_HUMANKS6A1_HUMANBioGRID, MINT21900206 details
ATX3_HUMANKITH_HUMANBioGRID, MINT21900206 details
ATX3_HUMANPRKN_HUMANBioGRID, IntAct20940148 22081612 24063750 29530980 30455355 details
ATX3_HUMANBECN1_HUMANBioGRID, IntAct28445460 details
ATX3_HUMANKAPCA_HUMANIntAct32814053 details
ATX3_HUMANTGFR2_HUMANIntAct32814053 details
ATX3_HUMANTCPZ_HUMANBioGRID, IntAct30455355 32814053 details
ATX3_HUMANSOX14_HUMANIntAct32814053 details
ATX3_HUMANCASP1_HUMANHPRD, IntAct32814053 9535906 details
ATX3_HUMANPDPK1_HUMANIntAct32814053 details
ATX3_HUMANSERPH_HUMANBioGRID, IntAct29111377 32814053 details
ATX3_HUMANPOC1A_HUMANIntAct32814053 details
ATX3_HUMANTEX11_HUMANBioGRID, HPRD, IntAct16713569 32814053 details
ATX3_HUMANSPA2L_HUMANIntAct32814053 details
ATX3_HUMANRN111_HUMANIntAct32814053 details
ATX3_HUMANFX4L6_HUMANIntAct32814053 details
ATX3_HUMANTERF2_HUMANIntAct32814053 details
ATX3_HUMANCASP3_HUMANIntAct32814053 details
ATX3_HUMANPIAS1_HUMANIntAct32814053 details
ATX3_HUMANWWP1_HUMANIntAct32814053 details
ATX3_HUMANSPAG8_HUMANIntAct32814053 details
ATX3_HUMANCCD17_HUMANIntAct32814053 details
ATX3_HUMANBSCL2_HUMANIntAct32814053 details
ATX3_HUMANRBPMS_HUMANIntAct32814053 details
ATX3_HUMANSYTL5_HUMANIntAct32814053 details
ATX3_HUMANTEX19_HUMANIntAct32814053 details
ATX3_HUMANPALS1_HUMANIntAct32814053 details
ATX3_HUMANRUAS1_HUMANIntAct32814053 details
ATX3_HUMANCDKAL_HUMANIntAct32814053 details
ATX3_HUMANFL2D_HUMANIntAct32814053 details
ATX3_HUMANCREB5_HUMANIntAct32814053 details
ATX3_HUMANH31_HUMANIntAct32814053 details
ATX3_HUMANPK3CA_HUMANIntAct32814053 details
ATX3_HUMANLYAM2_HUMANIntAct32814053 details
ATX3_HUMANHYPM_HUMANIntAct32814053 details
ATX3_HUMANHMMR_HUMANIntAct32814053 details
ATX3_HUMANTBX22_HUMANIntAct32814053 details
ATX3_HUMANPARVA_HUMANIntAct32814053 details
ATX3_HUMANRASF1_HUMANIntAct32814053 details
ATX3_HUMANMET7A_HUMANIntAct32814053 details
ATX3_HUMANDCR1B_HUMANIntAct32814053 details
ATX3_HUMANAAMDC_HUMANIntAct32814053 details
ATX3_HUMANLDH6B_HUMANIntAct32814053 details
ATX3_HUMANZMAT2_HUMANIntAct32814053 details
ATX3_HUMANTLR10_HUMANIntAct32814053 details
ATX3_HUMANTELO2_HUMANIntAct32814053 details
ATX3_HUMANFEZ2_HUMANIntAct32814053 details
ATX3_HUMANDLGP2_HUMANIntAct32814053 details
ATX3_HUMANARFG3_HUMANIntAct32814053 details
ATX3_HUMANMALT1_HUMANBioGRID, IntAct29111377 32814053 details
ATX3_HUMANSTK36_HUMANIntAct32814053 details
ATX3_HUMANS52A3_HUMANIntAct32814053 details
ATX3_HUMANPATZ1_HUMANIntAct32814053 details
ATX3_HUMANZHX3_HUMANIntAct32814053 details
ATX3_HUMANASIC4_HUMANIntAct32814053 details
ATX3_HUMANRNF31_HUMANIntAct32814053 details
ATX3_HUMANHDA10_HUMANIntAct32814053 details
ATX3_HUMANMYLIP_HUMANIntAct32814053 details
ATX3_HUMANNUP43_HUMANIntAct32814053 details
ATX3_HUMANVP37A_HUMANIntAct32814053 details
ATX3_HUMANZN366_HUMANIntAct32814053 details
ATX3_HUMANCG031_HUMANIntAct32814053 details
ATX3_HUMANCRLF3_HUMANIntAct32814053 details
ATX3_HUMANATL4_HUMANIntAct32814053 details
ATX3_HUMANCP054_HUMANIntAct32814053 details
ATX3_HUMANAB17C_HUMANIntAct32814053 details
ATX3_HUMANEDRF1_HUMANIntAct32814053 details
ATX3_HUMANCLPP_HUMANIntAct32814053 details
ATX3_HUMANNR0B2_HUMANIntAct32814053 details
ATX3_HUMANMKRN3_HUMANIntAct32814053 details
ATX3_HUMANUPAR_HUMANIntAct32814053 details
ATX3_HUMANFBLN1_HUMANIntAct32814053 details
ATX3_HUMANIBP4_HUMANIntAct32814053 details
ATX3_HUMANUNG_HUMANIntAct32814053 details
ATX3_HUMANCHLE_HUMANIntAct32814053 details
ATX3_HUMANFYN_HUMANIntAct32814053 details
ATX3_HUMANTYDP2_HUMANIntAct32814053 details
ATX3_HUMANMICA2_HUMANIntAct32814053 details
ATX3_HUMANARK72_HUMANIntAct32814053 details
ATX3_HUMANFANCG_HUMANIntAct32814053 details
ATX3_HUMANASB3_HUMANIntAct32814053 details
ATX3_HUMANMTF2_HUMANIntAct32814053 details
ATX3_HUMANKLH20_HUMANIntAct32814053 details
ATX3_HUMANLHX6_HUMANIntAct32814053 details
ATX3_HUMANGDAP1_HUMANIntAct32814053 details
ATX3_HUMANGORS2_HUMANIntAct32814053 details
ATX3_HUMANHDAC3_HUMANBioGRID17079677 29802126 details
ATX3_HUMANNCOR1_HUMANBioGRID17079677 details
ATX3_HUMANCBP_HUMANBioGRID12297501 17885668 30994454 details
ATX3_HUMANEP300_HUMANBioGRID12297501 details
ATX3_HUMANKAT2B_HUMANBioGRID12297501 details
ATX3_HUMANCHIP_HUMANBioGRID19153604 20943656 21625540 21855799 23696636 29111377 32401531 details
ATX3_HUMANUB2L3_HUMANBioGRID22081612 details
ATX3_HUMANUBE2S_HUMANBioGRID20622874 details
ATX3_HUMANTRAF6_HUMANBioGRID20622874 details
ATX3_HUMANCSK2B_HUMANBioGRID18839019 details
ATX3_HUMANNEDD8_HUMANBioGRID17935801 details
ATX3_HUMANRFFL_HUMANBioGRID22626734 details
ATX3_HUMANPJA1_HUMANBioGRID22626734 details
ATX3_HUMANTRI63_HUMANBioGRID22626734 details
ATX3_HUMANTRI55_HUMANBioGRID22626734 details
ATX3_HUMANTRI54_HUMANBioGRID22626734 details
ATX3_HUMANUBP21_HUMANBioGRID22626734 details
ATX3_HUMANGDIR1_HUMANBioGRID15952105 details
ATX3_HUMANASIC1_HUMANBioGRID15952105 details
ATX3_HUMANSUMO1_HUMANBioGRID15952105 28275011 details
ATX3_HUMANA4_HUMANBioGRID21832049 details
ATX3_HUMANHDAC6_HUMANBioGRID24685680 details
ATX3_HUMANTBB5_HUMANBioGRID24685680 30455355 details
ATX3_HUMANTBA1A_HUMANBioGRID24685680 details
ATX3_HUMANSQSTM_HUMANBioGRID25158237 details
ATX3_HUMANM3K1_HUMANBioGRID25260751 details
ATX3_HUMANPNKP_HUMANBioGRID25590633 30994454 details
ATX3_HUMANSMUF1_HUMANBioGRID20804422 details
ATX3_HUMANP53_HUMANBioGRID27851749 details
ATX3_HUMANCAN2_HUMANBioGRID27731380 28334907 details
ATX3_HUMANCHK1_HUMANBioGRID28180282 details
ATX3_HUMANCAN1_HUMANBioGRID28334907 details
ATX3_HUMANMLP3A_HUMANBioGRID30460066 31625269 details
ATX3_HUMANGBRAP_HUMANBioGRID31625269 details
ATX3_HUMANMLP3C_HUMANBioGRID31625269 details
ATX3_HUMANIMA1_HUMANBioGRID31107713 details
ATX3_HUMANUB2D3_HUMANBioGRID32401531 details
ATX3_HUMANUBE2W_HUMANBioGRID32401531 details
ATX3_HUMANUBB_HUMANBioGRID, HPRD, MINT12857950 16525503 29111377 details
ATX3_HUMANHAP1_HUMANBioGRID, UniProt21386698 30994454 details
ATX3_HUMANUBAC1_HUMANIntAct31413325 details
ATX3_HUMANMIC60_HUMANMINT31379806 details
ATX3_HUMANLTOR1_HUMANMINT31379806 details
ATX3_HUMANXRCC6_HUMANBioGRID17885668 30455355 details
ATX3_HUMANAMFR_HUMANBioGRID19661182 details
ATX3_HUMANFOXO4_HUMANBioGRID21536589 details
ATX3_HUMANPRS8_HUMANBioGRID17302910 30455355 details
ATX3_HUMANDNJB2_HUMANBioGRID21625540 details
ATX3_HUMANCREB1_HUMANBioGRID11572863 details
ATX3_HUMANPML_HUMANBioGRID11572863 details
ATX3_HUMANSPRTN_HUMANBioGRID23042605 details
ATX3_HUMANB2CL1_HUMANBioGRID23562578 details
ATX3_HUMANSYVN1_HUMANBioGRID24068323 details
ATX3_HUMANMGRN1_HUMANBioGRID24769000 details
ATX3_HUMANITCH_HUMANBioGRID24865853 details
ATX3_HUMANHS90A_HUMANBioGRID27851749 30455355 details
ATX3_HUMANMDC1_HUMANBioGRID28275011 details
ATX3_HUMANSDHB_HUMANBioGRID29111377 details
ATX3_HUMANNDUA4_HUMANBioGRID29111377 30455355 details
ATX3_HUMANHS105_HUMANBioGRID29111377 30455355 details
ATX3_HUMANHS71A_HUMANBioGRID29111377 details
ATX3_HUMANHS71B_HUMANBioGRID29111377 details
ATX3_HUMANDDB1_HUMANBioGRID28180282 30455355 details
ATX3_HUMANCUL1_HUMANBioGRID28180282 30685895 details
ATX3_HUMANCUL4A_HUMANBioGRID28180282 details
ATX3_HUMANTBB3_HUMANBioGRID28180282 details
ATX3_HUMANDYHC1_HUMANBioGRID28180282 30455355 details
ATX3_HUMANCASP7_HUMANBioGRID30455355 details
ATX3_HUMANTBA4A_HUMANBioGRID30455355 details
ATX3_HUMANHD_HUMANBioGRID30994454 details
ATX3_HUMANRPB1_HUMANBioGRID30994454 details
ATX3_HUMANDNLI3_HUMANBioGRID30994454 details
ATX3_HUMANTAF4_HUMANBioGRID30994454 details
ATX3_HUMANFBX33_HUMANBioGRID30685895 details
ATX3_HUMANPTC1_HUMANBioGRID31253779 details
ATX3_HUMANKLF4_HUMANBioGRID31563563 details
ATX3_HUMANLHX3_HUMANBioGRID23861948 details