Entity Details

Primary name LONP1
Entity type gene
Source Source Link

Details

PrimaryID9361
RefseqGeneNG_033142
SymbolLONP1
Namelon peptidase 1, mitochondrial
Chromosome19
Location19p13.3
TaxID9606
Statuslive
SourceGenomegenomic
SourceOriginnatural
CreationDate1999-09-20
ModificationDate2021-06-22

Ontological Relatives

UniProt IDsLONM_HUMAN

GO terms

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GOName
GO:0000002 mitochondrial genome maintenance
GO:0001018 mitochondrial promoter sequence-specific DNA binding
GO:0001666 response to hypoxia
GO:0003697 single-stranded DNA binding
GO:0003727 single-stranded RNA binding
GO:0004176 ATP-dependent peptidase activity
GO:0004252 serine-type endopeptidase activity
GO:0005524 ATP binding
GO:0005654 nucleoplasm
GO:0005739 mitochondrion
GO:0005759 mitochondrial matrix
GO:0005829 cytosol
GO:0006515 protein quality control for misfolded or incompletely synthesized proteins
GO:0007005 mitochondrion organization
GO:0007568 aging
GO:0009725 response to hormone
GO:0010044 response to aluminum ion
GO:0016020 membrane
GO:0016887 ATP hydrolysis activity
GO:0032042 mitochondrial DNA metabolic process
GO:0034599 cellular response to oxidative stress
GO:0042645 mitochondrial nucleoid
GO:0042802 identical protein binding
GO:0043531 ADP binding
GO:0043565 sequence-specific DNA binding
GO:0051131 chaperone-mediated protein complex assembly
GO:0051603 proteolysis involved in cellular protein catabolic process
GO:0051880 G-quadruplex DNA binding
GO:0070182 DNA polymerase binding
GO:0070407 oxidation-dependent protein catabolic process

Diseases

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Interactions

305 interactions

InteractorPartnerSourcesPublicationsLink
LONP1A2MBioGRID, IntAct21163940 details
LONP1CDC37BioGRID, IntAct21163940 details
LONP1CYP2C8BioGRID, IntAct21163940 details
LONP1ECSITBioGRID, IntAct21163940 details
LONP1LOXL4BioGRID, IntAct21163940 details
LONP1IFIT5BioGRID, IntAct21163940 details
LONP1IFIT3BioGRID, IntAct21163940 details
LONP1MAST1BioGRID, IntAct21163940 details
LONP1RNF32BioGRID, IntAct21163940 details
LONP1LONP1IntAct, MINT24520911 25574826 details
LONP1TFAMIntAct25574826 details
LONP1APOEBioGRID21163940 31536960 details
LONP1CDC42BioGRID31478661 details
LONP1MAP3K3IntAct14743216 details
LONP1TSC22D1IntAct17353931 details
LONP1MKLN1BioGRID, IntAct27173435 unassigned1312 details
LONP1C1QBPBioGRID22904065 32877691 details
LONP1MYCBioGRID, IntAct17314511 29467282 details
LONP1MMEBioGRID, IntAct17342744 details
LONP1USP2BioGRID, IntAct19615732 details
LONP1ESR2BioGRID, IntAct21182203 29509190 details
LONP1ATG101BioGRID, IntAct20562859 details
LONP1MRPL58BioGRID, MINT20186120 details
LONP1VCAM1IntAct22623428 details
LONP1ILKBioGRID, IntAct23455922 details
LONP1CUL1BioGRID, IntAct21145461 details
LONP1MAPK6BioGRID, IntAct26972000 details
LONP1JUNMINT25609649 details
LONP1SIRT4IntAct25525879 details
LONP1NDUFS7BioGRID, IntAct, MINT24344204 28514442 31536960 32877691 details
LONP1ATL3BioGRID, IntAct26496610 details
LONP1LRPPRCBioGRID, IntAct26496610 31536960 32877691 details
LONP1CEP162BioGRID, IntAct26638075 details
LONP1DCTN1BioGRID, IntAct26638075 details
LONP1RPGRIP1LBioGRID, IntAct26638075 details
LONP1CNTRLBioGRID, IntAct26638075 details
LONP1CEP164BioGRID, IntAct26638075 details
LONP1OFD1BioGRID, IntAct26638075 details
LONP1PPP2R2CBioGRID, IntAct28330616 details
LONP1MRPL4BioGRID, IntAct28514442 details
LONP1NEU4BioGRID, IntAct28514442 details
LONP1C9orf24BioGRID, IntAct28514442 details
LONP1KLHDC8ABioGRID, IntAct28514442 details
LONP1DCAF12L2BioGRID, IntAct28514442 details
LONP1UPF3ABioGRID, IntAct28514442 details
LONP1MRPS24BioGRID, IntAct28514442 32877691 details
LONP1RASL10BBioGRID, IntAct28514442 details
LONP1DCAF4BioGRID, IntAct28514442 details
LONP1GCATBioGRID, IntAct26186194 28514442 details
LONP1FOXRED1BioGRID, IntAct28514442 details
LONP1TEX45BioGRID, IntAct28514442 details
LONP1STPG3BioGRID, IntAct26186194 28514442 details
LONP1AURKAIP1BioGRID, IntAct29568061 details
LONP1HSPD1BioGRID, IntAct29568061 details
LONP1MGST3IntAct29568061 details
LONP1PDK1BioGRID, IntAct29568061 32877691 details
LONP1TRMT61BBioGRID, IntAct29568061 details
LONP1TUBG1BioGRID, IntAct23443559 29568061 details
LONP1MKI67BioGRID, IntAct26949251 details
LONP1CISD3IntAct27499296 details
LONP1NDUFA4IntAct27499296 details
LONP1SMARCB1IntAct30108113 details
LONP1STK38LIntAct30108113 details
LONP1NT5C3ABioGRID, IntAct30833792 details
LONP1SH3GL3BioGRID, IntAct31980649 details
LONP1PXNBioGRID, IntAct31980649 details
LONP1PRKCGBioGRID, IntAct31980649 details
LONP1HTRA4IntAct31470122 details
LONP1ZDHHC5UniProt31402609 details
LONP1NCBP2IntAct32960270 details
LONP1SOX2BioGRID, MINT23667531 details
LONP1NIPSNAP2BioGRID20562859 details
LONP1PSMA3BioGRID22079093 details
LONP1SIRT7BioGRID22586326 details
LONP1DYNC1H1BioGRID22939629 details
LONP1ITGA4BioGRID22623428 details
LONP1ADRB2BioGRID23798571 details
LONP1LATS2BioGRID24255178 details
LONP1CUL7BioGRID24711643 details
LONP1EGFRBioGRID24797263 28065597 details
LONP1CLPXBioGRID26344197 32877691 details
LONP1PSMC4BioGRID26344197 details
LONP1PSMC5BioGRID26344197 details
LONP1SF3B1BioGRID26344197 details
LONP1TATDN1BioGRID26344197 details
LONP1NTRK1BioGRID25921289 details
LONP1MTMR11BioGRID27880917 details
LONP1ARMC8BioGRID29911972 details
LONP1HDAC4BioGRID27684187 details
LONP1PIH1D1BioGRID28515276 details
LONP1EFTUD2BioGRID28515276 details
LONP1RECQL4BioGRID29229926 details
LONP1MRM1BioGRID29568061 details
LONP1VIRMABioGRID29507755 details
LONP1AMBRA1BioGRID30166453 details
LONP1RC3H2BioGRID30209976 details
LONP1NR2C2BioGRID30463901 details
LONP1NINBioGRID28718761 details
LONP1PORBioGRID31536960 details
LONP1NNTBioGRID31536960 32877691 details
LONP1NDUFS3BioGRID31536960 32877691 details
LONP1NDUFV1BioGRID31536960 32877691 details
LONP1ASPHBioGRID31536960 details
LONP1NDUFS8BioGRID31536960 32877691 details
LONP1CORO1CBioGRID31536960 details
LONP1CYC1BioGRID31536960 details
LONP1BCKDHABioGRID31536960 details
LONP1NDUFS1BioGRID31536960 32877691 details
LONP1HMOX2BioGRID31536960 details
LONP1ATP5F1BBioGRID31536960 32877691 details
LONP1UQCRC2BioGRID31536960 details
LONP1CANXBioGRID31536960 details
LONP1ATP6V1ABioGRID31536960 details
LONP1EMC8BioGRID31536960 details
LONP1P4HA1BioGRID31536960 details
LONP1UQCRHBioGRID31536960 details
LONP1ARMCX3BioGRID31536960 details
LONP1ATP2A2BioGRID31536960 details
LONP1RCN2BioGRID31536960 details
LONP1TPP1BioGRID31536960 details
LONP1EMC2BioGRID27342126 31536960 details
LONP1NDUFA9BioGRID31536960 32877691 details
LONP1LACTBBioGRID31536960 32877691 details
LONP1AGPSBioGRID31536960 details
LONP1EMC4BioGRID31536960 details
LONP1PON2BioGRID31536960 details
LONP1NDUFV2BioGRID31536960 32877691 details
LONP1SQORBioGRID31536960 details
LONP1EEF2BioGRID31536960 details
LONP1ATP6V1E1BioGRID31536960 details
LONP1VCPBioGRID31536960 details
LONP1LAMTOR2BioGRID31536960 details
LONP1BIRC3BioGRID30948266 details
LONP1PLEKHA4BioGRID31091453 details
LONP1MAGEA3BioGRID31267705 details
LONP1EMC1BioGRID27342126 details
LONP1IMMP1LBioGRID31617661 details
LONP1CITBioGRID31586073 details
LONP1ANLNBioGRID31586073 details
LONP1CHMP4BBioGRID31586073 details
LONP1KIF14BioGRID31586073 details
LONP1KIF20ABioGRID31586073 details
LONP1KIF23BioGRID31586073 details
LONP1PRC1BioGRID31586073 details
LONP1DEPDC1BBioGRID32203420 details
LONP1NGEFBioGRID32203420 details
LONP1ACAD9BioGRID32877691 details
LONP1AUHBioGRID32877691 details
LONP1C17orf80BioGRID32877691 details
LONP1GATD3BioGRID32877691 details
LONP1MCUR1BioGRID32877691 details
LONP1CCDC90BBioGRID32877691 details
LONP1FASTKD5BioGRID32877691 details
LONP1HINT2BioGRID32877691 details
LONP1ABCB7BioGRID32877691 details
LONP1ACAT1BioGRID32877691 details
LONP1ACOT1BioGRID32877691 details
LONP1ACOT2BioGRID32877691 details
LONP1AFG3L2BioGRID32877691 details
LONP1AK4BioGRID32877691 details
LONP1ALAS1BioGRID32877691 details
LONP1ATAD3ABioGRID32877691 details
LONP1ATP5MGBioGRID32877691 details
LONP1ATP5PBBioGRID32877691 details
LONP1ATP5PDBioGRID32877691 details
LONP1ATP5PFBioGRID32877691 details
LONP1ATP5POBioGRID32877691 details
LONP1ATPAF1BioGRID32877691 details
LONP1BCS1LBioGRID32877691 details
LONP1CARS2BioGRID32877691 details
LONP1CFL2BioGRID32877691 details
LONP1CLPBBioGRID32877691 details
LONP1COX2BioGRID32877691 details
LONP1COX4I1BioGRID32877691 details
LONP1COX5ABioGRID32877691 details
LONP1CSBioGRID32877691 34079125 details
LONP1DAP3BioGRID32877691 details
LONP1DLSTBioGRID32877691 details
LONP1ECHS1BioGRID32877691 details
LONP1ETFBBioGRID32877691 details
LONP1GATBBioGRID32877691 details
LONP1GCDHBioGRID32877691 details
LONP1GFM1BioGRID32877691 details
LONP1GLSBioGRID32877691 details
LONP1GRSF1BioGRID32877691 details
LONP1GUF1BioGRID32877691 details
LONP1HSD17B10BioGRID32877691 details
LONP1HSDL2BioGRID32877691 details
LONP1HSPE1BioGRID32877691 details
LONP1IARS2BioGRID32877691 details
LONP1IBA57BioGRID32877691 details
LONP1IMMTBioGRID32877691 details
LONP1LETM1BioGRID32877691 details
LONP1LYPLAL1BioGRID32877691 details
LONP1LYRM7BioGRID32877691 details
LONP1MDH2BioGRID32877691 details
LONP1MMABBioGRID32877691 details
LONP1MRPL12BioGRID32877691 details
LONP1MRPL20BioGRID32877691 details
LONP1MRPL21BioGRID32877691 details
LONP1MRPL3BioGRID32877691 details
LONP1MRPL43BioGRID32877691 details
LONP1MRPL44BioGRID32877691 details
LONP1MRPL50BioGRID32877691 details
LONP1MRPS10BioGRID32877691 details
LONP1MRPS14BioGRID32877691 details
LONP1MRPS17BioGRID32877691 details
LONP1MRPS18BBioGRID32877691 details
LONP1MRPS2BioGRID32877691 details
LONP1MRPS22BioGRID32877691 details
LONP1MRPS23BioGRID32877691 details
LONP1MRPS25BioGRID32877691 details
LONP1MRPS26BioGRID32877691 details
LONP1MRPS27BioGRID32877691 details
LONP1MRPS28BioGRID32877691 details
LONP1MRPS31BioGRID32877691 details
LONP1MRPS33BioGRID32877691 details
LONP1MRPS34BioGRID32877691 details
LONP1MRPS35BioGRID32877691 details
LONP1MRPS36BioGRID32877691 details
LONP1MRPS5BioGRID32877691 details
LONP1MRPS6BioGRID32877691 details
LONP1MRPS7BioGRID32877691 details
LONP1MRPS9BioGRID32877691 details
LONP1NDUFA12BioGRID32877691 details
LONP1NDUFA2BioGRID32877691 details
LONP1NDUFA5BioGRID32877691 details
LONP1NDUFA6BioGRID32877691 details
LONP1NDUFA7BioGRID32877691 details
LONP1NDUFAF2BioGRID32877691 details
LONP1NDUFAF3BioGRID32877691 details
LONP1NDUFAF4BioGRID32877691 details
LONP1NDUFAF7BioGRID32877691 details
LONP1NDUFS2BioGRID32877691 details
LONP1NDUFS4BioGRID32877691 details
LONP1NDUFS6BioGRID32877691 details
LONP1NDUFV3BioGRID32877691 details
LONP1NFS1BioGRID32877691 details
LONP1NIPSNAP1BioGRID32877691 details
LONP1NME4BioGRID32877691 details
LONP1OGDHBioGRID32877691 details
LONP1OXA1LBioGRID32877691 details
LONP1PDK3BioGRID32877691 details
LONP1PHBBioGRID32877691 details
LONP1PHB2BioGRID32877691 details
LONP1PNPLA8BioGRID32877691 details
LONP1PNPT1BioGRID32877691 details
LONP1POLDIP2BioGRID32877691 details
LONP1PTCD3BioGRID32877691 details
LONP1PYCR1BioGRID32877691 details
LONP1PYCR2BioGRID32877691 details
LONP1QRSL1BioGRID32877691 details
LONP1RAB13BioGRID32877691 details
LONP1RPS15ABioGRID32877691 details
LONP1RPS27LBioGRID32877691 details
LONP1RTN4IP1BioGRID32877691 details
LONP1SAMM50BioGRID32877691 details
LONP1SHMT2BioGRID32877691 details
LONP1SLC25A4BioGRID32877691 details
LONP1SLC2A1BioGRID32877691 details
LONP1SLC30A9BioGRID32877691 details
LONP1SLIRPBioGRID32877691 details
LONP1SSBP1BioGRID32877691 details
LONP1STOML2BioGRID32877691 details
LONP1SUCLA2BioGRID32877691 details
LONP1SUCLG1BioGRID32877691 details
LONP1TACO1BioGRID32877691 details
LONP1THEM4BioGRID32877691 details
LONP1TIMM44BioGRID32877691 details
LONP1TM9SF3BioGRID32877691 details
LONP1TRMT10CBioGRID32877691 details
LONP1UBAC2BioGRID32877691 details
LONP1VWA8BioGRID32877691 details
LONP1YARS1BioGRID32877691 details
LONP1METTL17BioGRID32877691 details
LONP1MRRFBioGRID32877691 details
LONP1MTG1BioGRID32877691 details
LONP1MTG2BioGRID32877691 details
LONP1MTIF2BioGRID32877691 details
LONP1MTRF1LBioGRID32877691 details
LONP1OCIAD1BioGRID32877691 details
LONP1PMPCABioGRID32877691 details
LONP1SLC25A12BioGRID32877691 details
LONP1SLC25A46BioGRID32877691 details
LONP1TBRG4BioGRID32877691 details
LONP1TRUB2BioGRID32877691 details
LONP1TSFMBioGRID32877691 details
LONP1EXD2BioGRID32877691 details
LONP1BRD4BioGRID32416067 details
LONP1WDR76BioGRID31353912 details
LONP1AARS2BioGRID34079125 details
LONP1ARF6BioGRID34079125 details
LONP1C11orf52BioGRID34079125 details
LONP1CLTABioGRID34079125 details
LONP1COILBioGRID34079125 details
LONP1COX8ABioGRID34079125 details
LONP1EMDBioGRID34079125 details
LONP1LAMTOR1BioGRID34079125 details
LONP1PDHA1BioGRID34079125 details
LONP1PEX3BioGRID34079125 details
LONP1RAB2ABioGRID34079125 details
LONP1SFXN1BioGRID34079125 details
LONP1SYNE3BioGRID34079125 details
LONP1TRAP1BioGRID34079125 details
LONP1TRIM25BioGRID29117863 details