Entity Details
Primary name |
AVIL_HUMAN |
Entity type |
UniProt |
Source |
Source Link |
Details
Accession | O75366 |
EntryName | AVIL_HUMAN |
FullName | Advillin |
TaxID | 9606 |
Evidence | evidence at protein level |
Length | 819 |
SequenceStatus | complete |
DateCreated | 2001-06-20 |
DateModified | 2021-06-02 |
Subcellular Location
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Subcellular Location |
Cell junction |
Cell projection |
Cytoplasm |
Domains
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Domain | Name | Category | Type |
IPR003128 | Villin headpiece | Domain | Domain |
IPR007122 | Villin/Gelsolin | Family | Family |
IPR007123 | Gelsolin-like domain | Domain | Domain |
IPR029006 | ADF-H/Gelsolin-like domain superfamily | Family | Homologous superfamily |
IPR036180 | Gelsolin-like domain superfamily | Family | Homologous superfamily |
IPR036886 | Villin headpiece domain superfamily | Family | Homologous superfamily |
Diseases
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Disease ID | Source | Name | Description |
618594 | OMIM | Nephrotic syndrome 21 (NPHS21) | A form of nephrotic syndrome, a renal disease clinically characterized by severe proteinuria, resulting in complications such as hypoalbuminemia, hyperlipidemia and edema. Kidney biopsies show non-specific histologic changes such as focal segmental glomerulosclerosis and diffuse mesangial proliferation. Some affected individuals have an inherited steroid-resistant form that progresses to end-stage renal failure. NPHS21 is an autosomal recessive, rapidly progressive, steroid-resistant form characterized by onset of kidney dysfunction in the first year of life. Some patients may have variable extra-renal manifestations. The disease is caused by variants affecting the gene represented in this entry. |
Interactions
1 interaction