Entity Details

Primary name P4ha1
Entity type gene
Source Source Link

Details

PrimaryID18451
RefseqGene
SymbolP4ha1
Nameprocollagen-proline, 2-oxoglutarate 4-dioxygenase (proline 4-hydroxylase), alpha 1 polypeptide
Chromosome10
Location10
TaxID10090
Statuslive
SourceGenomegenomic
SourceOriginnatural
CreationDate2000-05-24
ModificationDate2021-06-23

Ontological Relatives

UniProt IDsP4HA1_MOUSE

GO terms

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GOName
GO:0004656 procollagen-proline 4-dioxygenase activity
GO:0005506 iron ion binding
GO:0005739 mitochondrion
GO:0005783 endoplasmic reticulum
GO:0005788 endoplasmic reticulum lumen
GO:0016222 procollagen-proline 4-dioxygenase complex
GO:0016702 oxidoreductase activity, acting on single donors with incorporation of molecular oxygen, incorporation of two atoms of oxygen
GO:0018401 peptidyl-proline hydroxylation to 4-hydroxy-L-proline
GO:0030199 collagen fibril organization
GO:0031418 L-ascorbic acid binding
GO:0042802 identical protein binding
GO:0043231 intracellular membrane-bounded organelle

Diseases

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