Entity Details

Primary name MCCA_MOUSE
Entity type UniProt
Source Source Link

Details

AccessionQ99MR8
EntryNameMCCA_MOUSE
FullNameMethylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
TaxID10090
Evidenceevidence at protein level
Length717
SequenceStatuscomplete
DateCreated2002-03-05
DateModified2021-06-02

Ontological Relatives

GenesMccc1

GO terms

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GOName
GO:0002169 3-methylcrotonyl-CoA carboxylase complex, mitochondrial
GO:0004485 methylcrotonoyl-CoA carboxylase activity
GO:0005524 ATP binding
GO:0005739 mitochondrion
GO:0005743 mitochondrial inner membrane
GO:0005759 mitochondrial matrix
GO:0006552 leucine catabolic process
GO:0016421 CoA carboxylase activity
GO:0046872 metal ion binding
GO:1905202 methylcrotonoyl-CoA carboxylase complex

Subcellular Location

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Subcellular Location
Mitochondrion matrix

Domains

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DomainNameCategoryType
IPR000089 Biotin/lipoyl attachmentDomainDomain
IPR001882 Biotin-binding siteSiteBinding site
IPR005479 Carbamoyl-phosphate synthetase large subunit-like, ATP-binding domainDomainDomain
IPR005481 Biotin carboxylase-like, N-terminal domainDomainDomain
IPR005482 Biotin carboxylase, C-terminalDomainDomain
IPR011053 Single hybrid motifFamilyHomologous superfamily
IPR011054 Rudiment single hybrid motifFamilyHomologous superfamily
IPR011761 ATP-grasp foldDomainDomain
IPR011764 Biotin carboxylation domainDomainDomain
IPR013815 ATP-grasp fold, subdomain 1FamilyHomologous superfamily
IPR016185 Pre-ATP-grasp domain superfamilyFamilyHomologous superfamily

Diseases

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Interactions

1 interaction

InteractorPartnerSourcesPublicationsLink
MCCA_MOUSEHCD2_HUMANBioGRID22496890 details