Entity Details

Primary name MCCC1
Entity type gene
Source Source Link

Details

PrimaryID56922
RefseqGeneNG_008100
SymbolMCCC1
Namemethylcrotonyl-CoA carboxylase subunit 1
Chromosome3
Location3q27.1
TaxID9606
Statuslive
SourceGenomegenomic
SourceOriginnatural
CreationDate2001-02-27
ModificationDate2021-06-11

Ontological Relatives

UniProt IDsMCCA_HUMAN

GO terms

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GOName
GO:0002169 3-methylcrotonyl-CoA carboxylase complex, mitochondrial
GO:0004075 biotin carboxylase activity
GO:0004485 methylcrotonoyl-CoA carboxylase activity
GO:0005524 ATP binding
GO:0005739 mitochondrion
GO:0005759 mitochondrial matrix
GO:0005829 cytosol
GO:0006552 leucine catabolic process
GO:0006768 biotin metabolic process
GO:0009083 branched-chain amino acid catabolic process
GO:0009374 biotin binding
GO:0016421 CoA carboxylase activity
GO:0046872 metal ion binding
GO:1905202 methylcrotonoyl-CoA carboxylase complex

Diseases

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Interactions

2 interactions

InteractorPartnerSourcesPublicationsLink
MCCC1Prdm16MINT30462309 details
MCCC1MecomMINT30462309 details