Entity Details

Primary name ECHA_MOUSE
Entity type UniProt
Source Source Link

Details

AccessionQ8BMS1
EntryNameECHA_MOUSE
FullNameTrifunctional enzyme subunit alpha, mitochondrial
TaxID10090
Evidenceevidence at protein level
Length763
SequenceStatuscomplete
DateCreated2008-03-18
DateModified2021-06-02

Ontological Relatives

GenesHadha

GO terms

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GOName
GO:0000062 fatty-acyl-CoA binding
GO:0003857 3-hydroxyacyl-CoA dehydrogenase activity
GO:0003988 acetyl-CoA C-acyltransferase activity
GO:0004300 enoyl-CoA hydratase activity
GO:0005739 mitochondrion
GO:0005743 mitochondrial inner membrane
GO:0006635 fatty acid beta-oxidation
GO:0016507 mitochondrial fatty acid beta-oxidation multienzyme complex
GO:0016508 long-chain-enoyl-CoA hydratase activity
GO:0016509 long-chain-3-hydroxyacyl-CoA dehydrogenase activity
GO:0032868 response to insulin
GO:0035965 cardiolipin acyl-chain remodeling
GO:0042493 response to drug
GO:0042645 mitochondrial nucleoid
GO:0044877 protein-containing complex binding
GO:0051287 NAD binding
GO:0070403 NAD+ binding

Subcellular Location

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Subcellular Location
Mitochondrion
Mitochondrion inner membrane

Domains

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DomainNameCategoryType
IPR001753 Enoyl-CoA hydratase/isomeraseFamilyFamily
IPR006108 3-hydroxyacyl-CoA dehydrogenase, C-terminalDomainDomain
IPR006176 3-hydroxyacyl-CoA dehydrogenase, NAD bindingDomainDomain
IPR006180 3-hydroxyacyl-CoA dehydrogenase, conserved siteSiteConserved site
IPR008927 6-phosphogluconate dehydrogenase-like, C-terminal domain superfamilyFamilyHomologous superfamily
IPR012803 Fatty acid oxidation complex, alpha subunit, mitochondrialFamilyFamily
IPR018376 Enoyl-CoA hydratase/isomerase, conserved siteSiteConserved site
IPR029045 ClpP/crotonase-like domain superfamilyFamilyHomologous superfamily
IPR036291 NAD(P)-binding domain superfamilyFamilyHomologous superfamily

Diseases

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Interactions

1 interaction

InteractorPartnerSourcesPublicationsLink
ECHA_MOUSEHCD2_HUMANBioGRID22496890 details