Entity Details

Primary name EDEM1_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionQ92611
EntryNameEDEM1_HUMAN
FullNameER degradation-enhancing alpha-mannosidase-like protein 1
TaxID9606
Evidenceevidence at protein level
Length657
SequenceStatuscomplete
DateCreated2001-11-16
DateModified2021-06-02

Ontological Relatives

GenesEDEM1

GO terms

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GOName
GO:0004571 mannosyl-oligosaccharide 1,2-alpha-mannosidase activity
GO:0005509 calcium ion binding
GO:0005783 endoplasmic reticulum
GO:0005975 carbohydrate metabolic process
GO:0016235 aggresome
GO:0030176 integral component of endoplasmic reticulum membrane
GO:0030433 ubiquitin-dependent ERAD pathway
GO:0036498 IRE1-mediated unfolded protein response
GO:0036510 trimming of terminal mannose on C branch
GO:0044322 endoplasmic reticulum quality control compartment
GO:0045047 protein targeting to ER
GO:0051787 misfolded protein binding
GO:0097466 ubiquitin-dependent glycoprotein ERAD pathway
GO:1904154 positive regulation of retrograde protein transport, ER to cytosol
GO:1904382 mannose trimming involved in glycoprotein ERAD pathway

Subcellular Location

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Subcellular Location
Endoplasmic reticulum membrane

Domains

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DomainNameCategoryType
IPR001382 Glycoside hydrolase family 47FamilyFamily
IPR012341 Six-hairpin glycosidase-like superfamilyFamilyHomologous superfamily
IPR036026 Seven-hairpin glycosidasesFamilyHomologous superfamily
IPR044674 ER degradation-enhancing alpha-mannosidase-like protein 1/2/3FamilyFamily

Diseases

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