Entity Details

Primary name SPG7_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionQ9UQ90
EntryNameSPG7_HUMAN
FullNameParaplegin
TaxID9606
Evidenceevidence at protein level
Length795
SequenceStatuscomplete
DateCreated2001-04-27
DateModified2021-06-02

Ontological Relatives

GenesSPG7

GO terms

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GOName
GO:0004176 ATP-dependent peptidase activity
GO:0004222 metalloendopeptidase activity
GO:0005524 ATP binding
GO:0005739 mitochondrion
GO:0005743 mitochondrial inner membrane
GO:0005757 mitochondrial permeability transition pore complex
GO:0006508 proteolysis
GO:0006851 mitochondrial calcium ion transmembrane transport
GO:0007399 nervous system development
GO:0008053 mitochondrial fusion
GO:0008233 peptidase activity
GO:0008270 zinc ion binding
GO:0034982 mitochondrial protein processing
GO:0042407 cristae formation
GO:0046902 regulation of mitochondrial membrane permeability
GO:0051082 unfolded protein binding
GO:0065003 protein-containing complex assembly
GO:1902686 mitochondrial outer membrane permeabilization involved in programmed cell death

Subcellular Location

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Subcellular Location
Mitochondrion inner membrane

Domains

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DomainNameCategoryType
IPR000642 Peptidase M41DomainDomain
IPR003593 AAA+ ATPase domainDomainDomain
IPR003959 ATPase, AAA-type, coreDomainDomain
IPR005936 Peptidase, FtsHFamilyFamily
IPR011546 Peptidase M41, FtsH extracellularDomainDomain
IPR027417 P-loop containing nucleoside triphosphate hydrolaseFamilyHomologous superfamily
IPR037219 Peptidase M41-likeFamilyHomologous superfamily
IPR041569 AAA ATPase, AAA+ lid domainDomainDomain

Diseases

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Interactions

31 interactions

InteractorPartnerSourcesPublicationsLink
SPG7_HUMANTIF1B_HUMANBioGRID, HPRD, IntAct16169070 details
SPG7_HUMANRALY_HUMANBioGRID, HPRD, IntAct16169070 details
SPG7_HUMANPLS1_HUMANBioGRID, HPRD, IntAct16189514 details
SPG7_HUMANKR412_HUMANBioGRID, HPRD, IntAct16189514 details
SPG7_HUMANMDFI_HUMANBioGRID, HPRD, IntAct16189514 25416956 32296183 details
SPG7_HUMANMTUS2_HUMANBioGRID, IntAct, MINT21516116 25416956 details
SPG7_HUMANKRA59_HUMANBioGRID, MINT21516116 details
SPG7_HUMANPNMA1_HUMANBioGRID, IntAct, MINT21516116 25416956 32296183 details
SPG7_HUMANSTABP_HUMANBioGRID, IntAct21988832 details
SPG7_HUMANSPAS1_HUMANBioGRID, IntAct21988832 details
SPG7_HUMANMK06_HUMANBioGRID, MINT21900206 details
SPG7_HUMANPPIP1_HUMANBioGRID, IntAct25416956 details
SPG7_HUMANCCDB1_HUMANBioGRID, IntAct25416956 details
SPG7_HUMANKR107_HUMANBioGRID, IntAct25416956 details
SPG7_HUMANKR109_HUMANBioGRID, IntAct25416956 details
SPG7_HUMANPSME3_HUMANBioGRID, IntAct25416956 details
SPG7_HUMANHNRPK_HUMANBioGRID, IntAct25416956 32296183 details
SPG7_HUMANKHDR2_HUMANBioGRID, IntAct25416956 details
SPG7_HUMANK1C40_HUMANBioGRID, IntAct25416956 details
SPG7_HUMANNT2NA_HUMANBioGRID, IntAct25416956 32296183 details
SPG7_HUMANRBPMS_HUMANBioGRID, IntAct25416956 details
SPG7_HUMANLZTS2_HUMANBioGRID, IntAct25416956 details
SPG7_HUMANCRTP1_HUMANBioGRID, IntAct32296183 details
SPG7_HUMANHSF2B_HUMANBioGRID, IntAct32296183 details
SPG7_HUMANNT2NC_HUMANBioGRID, IntAct25416956 32296183 details
SPG7_HUMANBKRB2_HUMANBioGRID, MINT28298427 details
SPG7_HUMANLRIF1_HUMANBioGRID, HPRD16169070 details
SPG7_HUMANKR103_HUMANBioGRID25416956 details
SPG7_HUMANSASH1_HUMANBioGRID30480076 details
SPG7_HUMANRIF1_HUMANIntAct16169070 details
SPG7_HUMANELF3_HUMANIntAct17353931 details