Entity Details

Primary name AL4A1_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionP30038
EntryNameAL4A1_HUMAN
FullNameDelta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial
TaxID9606
Evidenceevidence at protein level
Length563
SequenceStatuscomplete
DateCreated1993-04-01
DateModified2021-06-02

Ontological Relatives

GenesALDH4A1

GO terms

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GOName
GO:0003842 1-pyrroline-5-carboxylate dehydrogenase activity
GO:0004029 aldehyde dehydrogenase (NAD+) activity
GO:0005739 mitochondrion
GO:0005759 mitochondrial matrix
GO:0005829 cytosol
GO:0006560 proline metabolic process
GO:0006562 proline catabolic process
GO:0009055 electron transfer activity
GO:0010133 proline catabolic process to glutamate
GO:0019470 4-hydroxyproline catabolic process
GO:0042802 identical protein binding
GO:0046487 glyoxylate metabolic process

Subcellular Location

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Subcellular Location
Mitochondrion matrix

Domains

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DomainNameCategoryType
IPR005931 Delta-1-pyrroline-5-carboxylate dehydrogenaseFamilyFamily
IPR015590 Aldehyde dehydrogenase domainDomainDomain
IPR016160 Aldehyde dehydrogenase, cysteine active siteSiteConserved site
IPR016161 Aldehyde/histidinol dehydrogenaseFamilyHomologous superfamily
IPR016162 Aldehyde dehydrogenase, N-terminalFamilyHomologous superfamily
IPR016163 Aldehyde dehydrogenase, C-terminalFamilyHomologous superfamily
IPR029510 Aldehyde dehydrogenase, glutamic acid active siteSiteConserved site

Diseases

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Drugs

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DrugNameSourceType
DB00157 NADHDrugbanksmall molecule

Interactions

5 interactions