Entity Details

Primary name ODBA_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionP12694
EntryNameODBA_HUMAN
FullName2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
TaxID9606
Evidenceevidence at protein level
Length445
SequenceStatuscomplete
DateCreated1989-10-01
DateModified2021-06-02

Ontological Relatives

GenesBCKDHA

GO terms

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GOName
GO:0003863 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring) activity
GO:0005739 mitochondrion
GO:0005759 mitochondrial matrix
GO:0005947 mitochondrial alpha-ketoglutarate dehydrogenase complex
GO:0009083 branched-chain amino acid catabolic process
GO:0016831 carboxy-lyase activity
GO:0046872 metal ion binding

Subcellular Location

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Subcellular Location
Mitochondrion matrix

Domains

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DomainNameCategoryType
IPR001017 Dehydrogenase, E1 componentDomainDomain
IPR029061 Thiamin diphosphate-binding foldFamilyHomologous superfamily
IPR034616 2-oxoisovalerate dehydrogenase subunit alphaFamilyFamily

Diseases

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Interactions

4 interactions