Entity Details

Primary name HEXA_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionP06865
EntryNameHEXA_HUMAN
FullNameBeta-hexosaminidase subunit alpha
TaxID9606
Evidenceevidence at protein level
Length529
SequenceStatuscomplete
DateCreated1988-01-01
DateModified2021-06-02

Ontological Relatives

GenesHEXA

GO terms

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GOName
GO:0004563 beta-N-acetylhexosaminidase activity
GO:0005829 cytosol
GO:0005975 carbohydrate metabolic process
GO:0006024 glycosaminoglycan biosynthetic process
GO:0006687 glycosphingolipid metabolic process
GO:0006689 ganglioside catabolic process
GO:0008375 acetylglucosaminyltransferase activity
GO:0016020 membrane
GO:0030207 chondroitin sulfate catabolic process
GO:0030214 hyaluronan catabolic process
GO:0042340 keratan sulfate catabolic process
GO:0042582 azurophil granule
GO:0043202 lysosomal lumen
GO:0043231 intracellular membrane-bounded organelle
GO:0046982 protein heterodimerization activity
GO:0070062 extracellular exosome
GO:0102148 N-acetyl-beta-D-galactosaminidase activity

Subcellular Location

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Subcellular Location
Lysosome

Domains

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DomainNameCategoryType
IPR015883 Glycoside hydrolase family 20, catalytic domainDomainDomain
IPR017853 Glycoside hydrolase superfamilyFamilyHomologous superfamily
IPR025705 Beta-hexosaminidaseFamilyFamily
IPR029018 Beta-hexosaminidase-like, domain 2FamilyHomologous superfamily
IPR029019 Beta-hexosaminidase, eukaryotic type, N-terminalDomainDomain

Diseases

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