Entity Details

Primary name RUSD4_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionQ96CM3
EntryNameRUSD4_HUMAN
FullNameMitochondrial RNA pseudouridine synthase RPUSD4
TaxID9606
Evidenceevidence at protein level
Length377
SequenceStatuscomplete
DateCreated2007-09-11
DateModified2021-06-02

Ontological Relatives

GenesRPUSD4

GO terms

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GOName
GO:0000049 tRNA binding
GO:0000455 enzyme-directed rRNA pseudouridine synthesis
GO:0003723 RNA binding
GO:0005654 nucleoplasm
GO:0005739 mitochondrion
GO:0005759 mitochondrial matrix
GO:0009982 pseudouridine synthase activity
GO:0035770 ribonucleoprotein granule
GO:0070131 positive regulation of mitochondrial translation
GO:0070902 mitochondrial tRNA pseudouridine synthesis
GO:1990400 mitochondrial ribosomal large subunit rRNA binding

Subcellular Location

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Subcellular Location
Mitochondrion matrix

Domains

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DomainNameCategoryType
IPR006145 Pseudouridine synthase, RsuA/RluA-likeDomainDomain
IPR006224 Pseudouridine synthase, RluC/RluD, conserved siteSiteConserved site
IPR020103 Pseudouridine synthase, catalytic domain superfamilyFamilyHomologous superfamily

Diseases

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