Entity Details

Primary name PYGM_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionP11217
EntryNamePYGM_HUMAN
FullNameGlycogen phosphorylase, muscle form
TaxID9606
Evidenceevidence at protein level
Length842
SequenceStatuscomplete
DateCreated1989-07-01
DateModified2021-06-02

Ontological Relatives

GenesPYGM

GO terms

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GOName
GO:0000166 nucleotide binding
GO:0005737 cytoplasm
GO:0005829 cytosol
GO:0005977 glycogen metabolic process
GO:0005980 glycogen catabolic process
GO:0008184 glycogen phosphorylase activity
GO:0030170 pyridoxal phosphate binding
GO:0070062 extracellular exosome
GO:0102250 linear malto-oligosaccharide phosphorylase activity
GO:0102499 SHG alpha-glucan phosphorylase activity

Subcellular Location

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Domains

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DomainNameCategoryType
IPR000811 Glycosyl transferase, family 35FamilyFamily
IPR011833 Glycogen/starch/alpha-glucan phosphorylaseFamilyFamily
IPR035090 Phosphorylase pyridoxal-phosphate attachment siteSiteConserved site

Diseases

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Disease IDSourceNameDescription
232600 OMIMGlycogen storage disease 5 (GSD5)A metabolic disorder resulting in myopathy characterized by exercise intolerance, cramps, muscle weakness and recurrent myoglobinuria. The disease is caused by variants affecting the gene represented in this entry.

Drugs

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DrugNameSourceType
DB00114 Pyridoxal phosphateDrugbanksmall molecule
DB01823 Beta-D-Glucopyranose SpirohydantoinDrugbanksmall molecule
DB01843 (5S,7R,8S,9S,10R)-3-Amino-8,9,10-trihydroxy-7-(hydroxymethyl)-6-oxa-1,3-diazaspiro[4.5]decane-2,4-dioneDrugbanksmall molecule
DB02007 alpha-D-glucose 6-phosphateDrugbanksmall molecule
DB02320 N-beta-D-glucopyranosylacetamideDrugbanksmall molecule
DB02348 Monofluorophosphate ionDrugbanksmall molecule
DB02379 Beta-D-GlucoseDrugbanksmall molecule
DB02447 3,8,9,10-tetrahydroxy-7-hydroxymethyl-6-oxa-1,3-diaza-spiro[4.5]decane-2,4-dioneDrugbanksmall molecule
DB02471 Nojirimycine TetrazoleDrugbanksmall molecule
DB02519 Indirubin-5-sulphonateDrugbanksmall molecule
DB02604 2-Deoxy-Glucose-6-PhosphateDrugbanksmall molecule
DB02719 C-(1-hydrogyl-beta-D-glucopyranosyl) formamideDrugbanksmall molecule
DB02720 alpha-D-glucopyranosyl-2-carboxylic acid amideDrugbanksmall molecule
DB02843 alpha-D-glucose-1-phosphateDrugbanksmall molecule
DB02964 8,9,10-Trihydroxy-7-hydroxymethyl-2-thioxo-6-oxa-1,3-diaza-spiro[4.5]decan-4-oneDrugbanksmall molecule
DB03067 4-{2,4-Bis[(3-Nitrobenzoyl)Amino]Phenoxy}Phthalic AcidDrugbanksmall molecule
DB03133 2-(Beta-D-Glucopyranosyl)-5-Methyl-1,2,3-BenzimidazoleDrugbanksmall molecule
DB03218 N-acetyl-N'-beta-D-glucopyranosyl ureaDrugbanksmall molecule
DB03250 2-(Beta-D-Glucopyranosyl)-5-Methyl-1,3,4-BenzothiazoleDrugbanksmall molecule
DB03286 C-(1-Azido-Alpha-D-Glucopyranosyl) FormamideDrugbanksmall molecule
DB03354 2-(Beta-D-Glucopyranosyl)-5-Methyl-1,3,4-OxadiazoleDrugbanksmall molecule
DB03383 CP-320626Drugbanksmall molecule
DB03392 (3,4,5-Trihydroxy-6-Hydroxymethyl-Tetrahydro-Pyran-2-Yl)-Phosphoramidic Acid Dimethyl EsterDrugbanksmall molecule
DB03479 8,9,10-trihydroxy-7-hydroxymethyl-3-methyl-6-oxa-1,3-diaza-spiro[4.5]decane-2,4-dioneDrugbanksmall molecule
DB03496 AlvocidibDrugbanksmall molecule
DB03657 1-deoxy-1-methoxycarbamido-beta-D-glucopyranoseDrugbanksmall molecule
DB03835 N-[(5S,7R,8S,9S,10R)-8,9,10-Trihydroxy-7-(hydroxymethyl)-2,4-dioxo-6-oxa-1,3-diazaspiro[4.5]dec-3-yl]acetamideDrugbanksmall molecule
DB04013 1-Deoxy-1-methoxycarbamido-beta-D-gluco-2-heptulopyranosonamideDrugbanksmall molecule
DB04044 4-{2-[(3-Nitrobenzoyl)Amino]Phenoxy}Phthalic AcidDrugbanksmall molecule
DB04055 2,3-Dicarboxy-4-(2-Chloro-Phenyl)-1-Ethyl-5-Isopropoxycarbonyl-6-Methyl-PyridiniumDrugbanksmall molecule
DB04083 N(6)-(pyridoxal phosphate)-L-lysineDrugbanksmall molecule
DB04195 Heptulose-2-PhosphateDrugbanksmall molecule
DB04295 N-(Benzoylcarbamoyl)-beta-D-glucopyranosylamineDrugbanksmall molecule
DB04522 DexfosfoserineDrugbanksmall molecule
DB04544 1-Deoxy-1-acetylamino-beta-D-gluco-2-heptulopyranosonamideDrugbanksmall molecule
DB04566 Inosinic AcidDrugbanksmall molecule
DB04642 7-{2,6-DICHLORO-4-[3-(2-CHLORO-BENZOYL)-UREIDO]-PHENOXY}-HEPTANOIC ACIDDrugbanksmall molecule
DB04643 4-{3-CHLORO-4-[3-(2,4-DICHLORO-BENZOYL)-UREIDO]-PHENOXY}-BUTYRIC ACIDDrugbanksmall molecule
DB04644 4-{4-[3-(2,4-DICHLORO-BENZOYL)-UREIDO]-2,3-DIMETHYL-PHENOXY}-BUTYRIC ACIDDrugbanksmall molecule
DB04645 5-{3-[3-(2,4-DICHLORO-BENZOYL)-UREIDO]-2-METHYL-PHENOXY}-PENTANOIC ACIDDrugbanksmall molecule
DB06986 2-CHLORO-N-[(1R,2R)-1-HYDROXY-2,3-DIHYDRO-1H-INDEN-2-YL]-6H-THIENO[2,3-B]PYRROLE-5-CARBOXAMIDEDrugbanksmall molecule
DB07066 2-CHLORO-N-[(3R)-2-OXO-1,2,3,4-TETRAHYDROQUINOLIN-3-YL]-6H-THIENO[2,3-B]PYRROLE-5-CARBOXAMIDEDrugbanksmall molecule
DB07792 (S)-2-CHLORO-N-(1-(2-(2-HYDROXYETHYLAMINO)-2-OXOETHYL)-2-OXO-1,2,3,4-TETRAHYDROQUINOLIN-3-YL)-6H-THIENO[2,3-B]PYRROLE-5-CARBOXAMIDEDrugbanksmall molecule
DB07793 (2S)-N-[(3S)-1-(2-AMINO-2-OXOETHYL)-2-OXO-1,2,3,4-TETRAHYDROQUINOLIN-3-YL]-2-CHLORO-2H-THIENO[2,3-B]PYRROLE-5-CARBOXAMIDEDrugbanksmall molecule
DB07807 (3R,4R,5R)-5-(HYDROXYMETHYL)-1-(3-PHENYLPROPYL)PIPERIDINE-3,4-DIOLDrugbanksmall molecule
DB07949 ({[(3E)-2'-Oxo-2',7'-dihydro-2,3'-biindol-3(7H)-ylidene]amino}oxy)acetic acidDrugbanksmall molecule
DB08151 (5R,7R,8S,9S,10R)-7-(hydroxymethyl)-3-phenyl-1,6-dioxa-2-azaspiro[4.5]dec-2-ene-8,9,10-triolDrugbanksmall molecule
DB08322 2-DEOXY-3,4-BIS-O-[3-(4-HYDROXYPHENYL)PROPANOYL]-L-THREO-PENTARIC ACIDDrugbanksmall molecule
DB08500 (3S,5R,7R,8S,9S,10R)-7-(hydroxymethyl)-3-(2-naphthyl)-1,6-dioxa-2-azaspiro[4.5]decane-8,9,10-triolDrugbanksmall molecule
DB08503 (3S,5R,7R,8S,9S,10R)-7-(hydroxymethyl)-3-(4-methylphenyl)-1,6-dioxa-2-azaspiro[4.5]decane-8,9,10-triolDrugbanksmall molecule

Interactions

33 interactions

InteractorPartnerSourcesPublicationsLink
PYGM_HUMANPOMP_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANCBPC1_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANARI1B_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANMRCKB_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANCLAP2_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANDYN2_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANF110A_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANNIPS2_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANIGBP1_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANINT4_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANLMNA_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANMYOME_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANPPR3B_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANSRP72_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANTRI54_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANTRI55_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANTITIN_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANWWP1_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANSGCG_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANTPC2A_HUMANBioGRID, IntAct23414517 details
PYGM_HUMANAAKB2_HUMANBioGRID, IntAct24722188 25416956 32296183 details
PYGM_HUMANNTAQ1_HUMANBioGRID, IntAct25416956 31515488 details
PYGM_HUMANPYGL_HUMANBioGRID, IntAct32296183 details
PYGM_HUMANPYGB_HUMANBioGRID, IntAct32296183 details
PYGM_HUMANS10A1_HUMANBioGRID, HPRD12804600 details
PYGM_HUMANTRI63_HUMANBioGRID, HPRD18468620 details
PYGM_HUMANTOP1_HUMANBioGRID12549820 details
PYGM_HUMANPP2AA_HUMANBioGRID11983168 details
PYGM_HUMANPP1A_HUMANBioGRID23088536 details
PYGM_HUMANTPC2B_HUMANBioGRID23414517 details
PYGM_HUMANM3K3_HUMANIntAct14743216 details
PYGM_HUMANINP5K_HUMANIntAct17353931 details
PYGM_HUMANPYGM_HUMANHPRD10949035 details