Entity Details

Primary name IVD_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionP26440
EntryNameIVD_HUMAN
FullNameIsovaleryl-CoA dehydrogenase, mitochondrial
TaxID9606
Evidenceevidence at protein level
Length426
SequenceStatuscomplete
DateCreated1992-08-01
DateModified2021-06-02

Ontological Relatives

GenesIVD

GO terms

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GOName
GO:0004085 butyryl-CoA dehydrogenase activity
GO:0005759 mitochondrial matrix
GO:0006552 leucine catabolic process
GO:0008470 isovaleryl-CoA dehydrogenase activity
GO:0009083 branched-chain amino acid catabolic process
GO:0031966 mitochondrial membrane
GO:0033539 fatty acid beta-oxidation using acyl-CoA dehydrogenase
GO:0042802 identical protein binding
GO:0050660 flavin adenine dinucleotide binding

Subcellular Location

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Subcellular Location
Mitochondrion matrix

Domains

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DomainNameCategoryType
IPR006089 Acyl-CoA dehydrogenase, conserved siteSiteConserved site
IPR006091 Acyl-CoA oxidase/dehydrogenase, central domainDomainDomain
IPR009075 Acyl-CoA dehydrogenase/oxidase C-terminalDomainDomain
IPR009100 Acyl-CoA dehydrogenase/oxidase, N-terminal and middle domain superfamilyFamilyHomologous superfamily
IPR013786 Acyl-CoA dehydrogenase/oxidase, N-terminalDomainDomain
IPR034183 Isovaleryl-CoA dehydrogenaseFamilyFamily
IPR036250 Acyl-CoA dehydrogenase-like, C-terminalFamilyHomologous superfamily
IPR037069 Acyl-CoA dehydrogenase/oxidase, N-terminal domain superfamilyFamilyHomologous superfamily

Diseases

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Drugs

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DrugNameSourceType
DB03147 Flavin adenine dinucleotideDrugbanksmall molecule
DB04036 Coenzyme A persulfideDrugbanksmall molecule