Entity Details

Primary name MMAA_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionQ8IVH4
EntryNameMMAA_HUMAN
FullNameMethylmalonic aciduria type A protein, mitochondrial
TaxID9606
Evidenceevidence at protein level
Length418
SequenceStatuscomplete
DateCreated2003-11-07
DateModified2021-06-02

Ontological Relatives

GenesMMAA

GO terms

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GOName
GO:0003924 GTPase activity
GO:0005525 GTP binding
GO:0005737 cytoplasm
GO:0005739 mitochondrion
GO:0005759 mitochondrial matrix
GO:0009235 cobalamin metabolic process
GO:0019626 short-chain fatty acid catabolic process
GO:0042802 identical protein binding
GO:0042803 protein homodimerization activity

Subcellular Location

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Subcellular Location
Cytoplasm
Mitochondrion

Domains

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DomainNameCategoryType
IPR005129 SIMIBI class G3E GTPase, ArgK/MeaBFamilyFamily
IPR027417 P-loop containing nucleoside triphosphate hydrolaseFamilyHomologous superfamily

Diseases

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Drugs

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DrugNameSourceType
DB00115 CyanocobalaminDrugbanksmall molecule
DB00200 HydroxocobalaminDrugbanksmall molecule

Interactions

2 interactions

InteractorPartnerSourcesPublicationsLink
MMAA_HUMANMUTA_HUMANBioGRID, HPRD, IntAct16641088 20876572 28497574 details
MMAA_HUMANMMAA_HUMANBioGRID, IntAct20876572 details