Entity Details

Primary name ODPX_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionO00330
EntryNameODPX_HUMAN
FullNamePyruvate dehydrogenase protein X component, mitochondrial
TaxID9606
Evidenceevidence at protein level
Length501
SequenceStatuscomplete
DateCreated1999-07-15
DateModified2021-06-02

Ontological Relatives

GenesPDHX

GO terms

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GOName
GO:0005739 mitochondrion
GO:0005759 mitochondrial matrix
GO:0006090 pyruvate metabolic process
GO:0016746 acyltransferase activity
GO:0045254 pyruvate dehydrogenase complex
GO:0061732 mitochondrial acetyl-CoA biosynthetic process from pyruvate

Subcellular Location

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Subcellular Location
Mitochondrion matrix

Domains

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DomainNameCategoryType
IPR000089 Biotin/lipoyl attachmentDomainDomain
IPR001078 2-oxoacid dehydrogenase acyltransferase, catalytic domainDomainDomain
IPR003016 2-oxo acid dehydrogenase, lipoyl-binding siteSiteBinding site
IPR004167 Peripheral subunit-binding domainDomainDomain
IPR011053 Single hybrid motifFamilyHomologous superfamily
IPR023213 Chloramphenicol acetyltransferase-like domain superfamilyFamilyHomologous superfamily
IPR036625 E3-binding domain superfamilyFamilyHomologous superfamily

Diseases

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