Entity Details

Primary name MUTA_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionP22033
EntryNameMUTA_HUMAN
FullNameMethylmalonyl-CoA mutase, mitochondrial
TaxID9606
Evidenceevidence at protein level
Length750
SequenceStatuscomplete
DateCreated1991-08-01
DateModified2021-06-02

Ontological Relatives

GenesMMUT

GO terms

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GOName
GO:0003924 GTPase activity
GO:0004494 methylmalonyl-CoA mutase activity
GO:0005737 cytoplasm
GO:0005739 mitochondrion
GO:0005759 mitochondrial matrix
GO:0009235 cobalamin metabolic process
GO:0009791 post-embryonic development
GO:0019626 short-chain fatty acid catabolic process
GO:0031419 cobalamin binding
GO:0042802 identical protein binding
GO:0042803 protein homodimerization activity
GO:0043547 positive regulation of GTPase activity
GO:0046872 metal ion binding
GO:0050667 homocysteine metabolic process
GO:0072341 modified amino acid binding

Subcellular Location

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Subcellular Location
Cytoplasm
Mitochondrion
Mitochondrion matrix

Domains

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DomainNameCategoryType
IPR006098 Methylmalonyl-CoA mutase, alpha chain, catalyticDomainDomain
IPR006099 Methylmalonyl-CoA mutase, alpha/beta chain, catalyticDomainDomain
IPR006158 Cobalamin (vitamin B12)-binding domainDomainDomain
IPR006159 Methylmalonyl-CoA mutase, C-terminalDomainDomain
IPR016176 Cobalamin (vitamin B12)-dependent enzyme, catalyticFamilyHomologous superfamily
IPR036724 Cobalamin-binding domain superfamilyFamilyHomologous superfamily

Diseases

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Drugs

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DrugNameSourceType
DB00115 CyanocobalaminDrugbanksmall molecule
DB00200 HydroxocobalaminDrugbanksmall molecule

Interactions

4 interactions