Entity Details

Primary name ECHB_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionP55084
EntryNameECHB_HUMAN
FullNameTrifunctional enzyme subunit beta, mitochondrial
TaxID9606
Evidenceevidence at protein level
Length474
SequenceStatuscomplete
DateCreated1996-10-01
DateModified2021-06-02

Ontological Relatives

GenesHADHB

GO terms

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GOName
GO:0003723 RNA binding
GO:0003857 3-hydroxyacyl-CoA dehydrogenase activity
GO:0003988 acetyl-CoA C-acyltransferase activity
GO:0004300 enoyl-CoA hydratase activity
GO:0005739 mitochondrion
GO:0005740 mitochondrial envelope
GO:0005741 mitochondrial outer membrane
GO:0005743 mitochondrial inner membrane
GO:0005783 endoplasmic reticulum
GO:0006635 fatty acid beta-oxidation
GO:0035965 cardiolipin acyl-chain remodeling
GO:0042645 mitochondrial nucleoid
GO:0050633 acetyl-CoA C-myristoyltransferase activity

Subcellular Location

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Subcellular Location
Endoplasmic reticulum
Mitochondrion
Mitochondrion inner membrane
Mitochondrion outer membrane

Domains

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DomainNameCategoryType
IPR002155 ThiolaseFamilyFamily
IPR016039 Thiolase-likeFamilyHomologous superfamily
IPR020610 Thiolase, active siteSiteActive site
IPR020613 Thiolase, conserved siteSiteConserved site
IPR020615 Thiolase, acyl-enzyme intermediate active siteSiteActive site
IPR020616 Thiolase, N-terminalDomainDomain
IPR020617 Thiolase, C-terminalDomainDomain

Diseases

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