Entity Details

Primary name FBN3_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionQ75N90
EntryNameFBN3_HUMAN
FullNameFibrillin-3
TaxID9606
Evidenceevidence at transcript level
Length2809
SequenceStatuscomplete
DateCreated2004-07-19
DateModified2021-06-02

Ontological Relatives

GenesFBN3

GO terms

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GOName
GO:0005201 extracellular matrix structural constituent
GO:0005509 calcium ion binding
GO:0005576 extracellular region
GO:0009653 anatomical structure morphogenesis
GO:0031012 extracellular matrix
GO:0062023 collagen-containing extracellular matrix

Subcellular Location

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Subcellular Location
Secreted

Domains

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DomainNameCategoryType
IPR000152 EGF-type aspartate/asparagine hydroxylation sitePTMPTM
IPR000742 EGF-like domainDomainDomain
IPR001881 EGF-like calcium-binding domainDomainDomain
IPR009030 Growth factor receptor cysteine-rich domain superfamilyFamilyHomologous superfamily
IPR011398 FibrillinFamilyFamily
IPR017878 TB domainDomainDomain
IPR018097 EGF-like calcium-binding, conserved siteSiteConserved site
IPR026823 Complement Clr-like EGF domainDomainDomain
IPR036773 TGF-beta binding (TB) domain superfamilyFamilyHomologous superfamily
IPR040872 Fibrillin 1, unique N-terminal domainDomainDomain

Diseases

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Drugs

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DrugNameSourceType
DB11093 Calcium citrateDrugbanksmall molecule
DB11348 Calcium PhosphateDrugbanksmall molecule
DB14481 Calcium phosphate dihydrateDrugbanksmall molecule