Entity Details

Primary name DSG4_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionQ86SJ6
EntryNameDSG4_HUMAN
FullNameDesmoglein-4
TaxID9606
Evidenceevidence at transcript level
Length1040
SequenceStatuscomplete
DateCreated2005-03-01
DateModified2021-06-02

Ontological Relatives

GenesDSG4

GO terms

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GOName
GO:0001533 cornified envelope
GO:0001942 hair follicle development
GO:0005509 calcium ion binding
GO:0005886 plasma membrane
GO:0005911 cell-cell junction
GO:0007156 homophilic cell adhesion via plasma membrane adhesion molecules
GO:0016021 integral component of membrane
GO:0030057 desmosome
GO:0030509 BMP signaling pathway
GO:0031424 keratinization
GO:0070268 cornification
GO:0098609 cell-cell adhesion

Subcellular Location

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Subcellular Location
Cell junction
Cell membrane

Domains

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DomainNameCategoryType
IPR000233 Cadherin, cytoplasmic domainDomainDomain
IPR002126 Cadherin-likeDomainDomain
IPR009122 Desmosomal cadherinFamilyFamily
IPR009123 DesmogleinFamilyFamily
IPR015919 Cadherin-like superfamilyFamilyHomologous superfamily
IPR020894 Cadherin conserved siteSiteConserved site
IPR027397 Catenin binding domain superfamilyFamilyHomologous superfamily

Diseases

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Disease IDSourceNameDescription
607903 OMIMHypotrichosis 6 (HYPT6)A condition characterized by the presence of less than the normal amount of hair and abnormal hair follicles and shafts, which are thin and atrophic. The disorder affects the trunk and extremities as well as the scalp, and the eyebrows and eyelashes may also be involved, whereas beard, pubic, and axillary hairs are largely spared. In addition, patients can develop hyperkeratotic follicular papules, erythema, and pruritus in affected areas. In some patients with congenital hypotrichosis, monilethrix-like hairs showing elliptical nodes have been observed. HYPT6 inheritance is autosomal recessive. The disease is caused by variants affecting the gene represented in this entry.

Interactions

0 interactions

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