Entity Details

Primary name TTC7A_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionQ9ULT0
EntryNameTTC7A_HUMAN
FullNameTetratricopeptide repeat protein 7A
TaxID9606
Evidenceevidence at protein level
Length858
SequenceStatuscomplete
DateCreated2001-06-01
DateModified2021-06-02

Ontological Relatives

GenesTTC7A

GO terms

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GOName
GO:0005737 cytoplasm
GO:0005886 plasma membrane
GO:0006879 cellular iron ion homeostasis
GO:0030097 hemopoiesis
GO:0046854 phosphatidylinositol phosphate biosynthetic process
GO:0072659 protein localization to plasma membrane

Subcellular Location

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Subcellular Location
Cell membrane
Cytoplasm

Domains

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DomainNameCategoryType
IPR011990 Tetratricopeptide-like helical domain superfamilyFamilyHomologous superfamily
IPR019734 Tetratricopeptide repeatRepeatRepeat
IPR026900 Tetratricopeptide repeat protein 7AFamilyFamily

Diseases

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Disease IDSourceNameDescription
243150 OMIMGastrointestinal defects and immunodeficiency syndrome (GIDID)A rare, severe congenital disorder in which obstructions occur at various levels throughout the small and large intestines, ultimately leading to organ failure. Surgical interventions are palliative but do not provide long-term survival. Severe immunodeficiency may be associated with the phenotype. The disease is caused by variants affecting the gene represented in this entry. Phenotypic variations have been observed: the mildest case show intestinal aberrations consisting of bloody diarrhea, apoptotic enterocolitis, and acute graft-versus-host disease- (GVHD)-like symptoms, but no atresias (PubMed:25546680). Other patients show multiple intestinal atresias, some being associated with immunodeficiency syndrome, while other do not show immunodeficiency defects (PubMed:23423984).

Interactions

0 interactions

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