Entity Details

Primary name HUTH_HUMAN
Entity type UniProt
Source Source Link

Details

AccessionP42357
EntryNameHUTH_HUMAN
FullNameHistidine ammonia-lyase
TaxID9606
Evidenceevidence at protein level
Length657
SequenceStatuscomplete
DateCreated1995-11-01
DateModified2021-06-02

Ontological Relatives

GenesHAL

GO terms

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GOName
GO:0004397 histidine ammonia-lyase activity
GO:0005829 cytosol
GO:0006548 histidine catabolic process
GO:0016841 ammonia-lyase activity
GO:0019556 histidine catabolic process to glutamate and formamide
GO:0019557 histidine catabolic process to glutamate and formate

Subcellular Location

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Domains

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DomainNameCategoryType
IPR001106 Aromatic amino acid lyaseFamilyFamily
IPR005921 Histidine ammonia-lyaseFamilyFamily
IPR008948 L-Aspartase-likeFamilyHomologous superfamily
IPR021922 Par3/HAL, N-terminalDomainDomain
IPR022313 Phenylalanine/histidine ammonia-lyases, active siteSiteActive site
IPR024083 Fumarase/histidase, N-terminalFamilyHomologous superfamily

Diseases

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Disease IDSourceNameDescription
235800 OMIMHistidinemia (HISTID)Autosomal recessive disease characterized by increased histidine and histamine as well as decreased urocanic acid in body fluids. The disease is caused by variants affecting the gene represented in this entry.

Drugs

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DrugNameSourceType
DB00117 HistidineDrugbanksmall molecule

Interactions

0 interactions

InteractorPartnerSourcesPublicationsLink