Entity Details
Details
PrimaryID | 170825 |
RefseqGene | |
Symbol | GSX2 |
Name | GS homeobox 2 |
Chromosome | 4 |
Location | 4q12 |
TaxID | 9606 |
Status | live |
SourceGenome | genomic |
SourceOrigin | natural |
CreationDate | 2002-02-23 |
ModificationDate | 2021-06-11 |
Diseases
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Disease ID | Source | Name | Description |
618646 | OMIM | Diencephalic-mesencephalic junction dysplasia syndrome 2 (DMJDS2) | An autosomal recessive neurodevelopmental disorder with onset at birth, characterized by severe global developmental delay, hypotonia, spastic tetraparesis, generalized dystonia and severe intellectual impairment. Brain imaging shows a unique brain malformation characterized by agenesis of putamina and globi pallidi, dysgenesis of the caudate nuclei, olfactory bulbs hypoplasia, and anomaly of the diencephalic-mesencephalic junction with abnormal corticospinal tract course. The disease is caused by variants affecting the gene represented in this entry. |
Interactions
1 interaction